| Age (years) mean ± SD | 36 ± 10 |
| Age at exam (years) mean ± SD | 21 ± 8 |
| Age at onset (years) mean ± SD | 15 ± 6 |
| Sex (male) | 49/72 (68%) |
| Consanguinity | |
| ¾ FA | 16/33 (48.5%) |
| ¾ AVED | 7/11 (63.6%) |
| Gait | |
| ¾ Walk without help | 40/72 (55.6%) |
| ¾ Confined to bed | 4/72 (5.6%) |
| Abolished tendon reflexes | 63/72 (87.5%) |
| LL weakness | 45/72 (62.5%) |
| UL weakness | 13/72 (18.1%) |
| Dysathria | 53/72 (73.6%) |
| BB signs | 46/72 (63.9%) |
| Amyotrophy | 10/72 (14%) |
| Normal Glycemia | 36/37 (97%) |
| Lipidogram abnormal | 7/37 (18%) |
| CT scan | |
| ¾ Normal | 13/29 (44.8%) |
| ¾ Atrophy | 16/29 (55.1%) |